Intestinal Subocclusion Due to Rapunzel Syndrome in a Female with Cerebral Palsy

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Francisco Javier Hernandez Álvarez
Nora Lis Flores Olmos
Carlos Eliuth Cortés Sanchez
Andres Aguilar Arroyo
Irving Othoniel Zavala Cid

Abstract


Rapunzel syndrome is a rare variant of trichobezoar characterized by a hair mass extending from the stomach into the duodenum. Management depends on the severity of clinical presentation and the bezoar's size and location, with surgery often being the preferred approach. This condition predominantly affects adolescent females with psychiatric disorders or neurodevelopmental delays, particularly those exhibiting trichotillomania and trichophagia. We report the case of a 19-year-old female with cerebral palsy who presented with nonspecific diffuse abdominal pain, nausea, vomiting, and episodes of constipation. Imaging studies, including ultrasound and computed tomography, suggested the presence of a trichobezoar.


Clinicians should maintain a high index of suspicion for trichobezoar in adolescents with signs of partial or complete intestinal obstruction, especially when associated with psychiatric comorbidities and a known history of hair-pulling behaviors.


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How to Cite
Hernandez Álvarez, Francisco Javier, Nora Lis Flores Olmos, Carlos Eliuth Cortés Sanchez, Andres Aguilar Arroyo, and Irving Othoniel Zavala Cid. 2025. “Intestinal Subocclusion Due to Rapunzel Syndrome in a Female With Cerebral Palsy”. International Journal of Medical Science and Clinical Research Studies 5 (07):1207-10. https://doi.org/10.47191/ijmscrs/v5-i07-31.
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